Salla Disease and Lysosomal Sugar Transport

Jonas, Adam J.

Abstract

Funding Agency

• Agency: National Institute of Health (NIH)
• Institute: National Institute of Diabetes and Digestive and Kidney Diseases (NIDDK)
• Type: Research Project (R01)
• Project #: 5R01DK037403-04
• Application #: 3236286
• Study Section: Biochemistry Study Section (BIO)
• Project Start: 1988-09-01
• Project End: 1991-08-31
• Budget Start: 1989-09-01
• Budget End: 1991-08-31
• Support Year: 4
• Fiscal Year: 1989

Institution

• Name: Los Angeles County Harbor-UCLA Medical Center
• City: Torrance
• State: CA
• Country: United States
• Zip Code: 90509

Publications

Koetters, P J; Chou, H F; Jonas, A J (1995) Lysosomal sulfate transport: inhibitor studies. Biochim Biophys Acta 1235:79-84

Vadgama, J V; Chang, K; Kopple, J D et al. (1991) Characteristics of taurine transport in rat liver lysosomes. J Cell Physiol 147:447-54

Idriss, J M; Jonas, A J (1991) Vitamin B12 transport by rat liver lysosomal membrane vesicles. J Biol Chem 266:9438-41

Jonas, A J; Jobe, H (1990) N-acetyl-D-glucosamine countertransport in lysosomal membrane vesicles. Biochem J 268:41-5

Jonas, A J; Conrad, P; Jobe, H (1990) Neutral-sugar transport by rat liver lysosomes. Biochem J 272:323-6

Jonas, A J; Jobe, H (1990) Sulfate transport by rat liver lysosomes. J Biol Chem 265:17545-9

Jonas, A J; Butler, I J (1989) Circumvention of defective neutral amino acid transport in Hartnup disease using tryptophan ethyl ester. J Clin Invest 84:200-4

Jonas, A J; Speller, R J (1989) Stearylamine permeabilizes the lysosomal membrane to cystine and sialic acid. Biochim Biophys Acta 984:257-61

Jonas, A J; Speller, R J; Conrad, P B et al. (1989) Transport of N-acetyl-D-glucosamine and N-acetyl-D-galactosamine by rat liver lysosomes. J Biol Chem 264:4953-6

Jonas, A J; Lin, S N; Conley, S B et al. (1989) Urine glyceraldehyde excretion is elevated in the renal Fanconi syndrome. Kidney Int 35:99-104