Agency
National Institute of Health (NIH)
Institute
National Institute of Neurological Disorders and Stroke (NINDS)
Type
Research Project (R01)
Project #
5R01NS032348-03
Application #
2037724
Study Section
Neurological Sciences Subcommittee 1 (NLS)
Program Officer
Small, Judy A
Project Start
1994-02-28
Project End
1998-01-31
Budget Start
1996-02-01
Budget End
1998-01-31
Support Year
3
Fiscal Year
1996
Total Cost
Indirect Cost
Name
Lincoln University
Department
Type
DUNS #
592214472
City
Canterbury
State
Country
New Zealand
Zip Code
8000
Cook, R W; Jolly, R D; Palmer, D N et al. (2002) Neuronal ceroid lipofuscinosis in Merino sheep. Aust Vet J 80:292-7
Oswald, M J; Palmer, D N; Damak, S (1999) Splicing variants in sheep CLN3, the gene underlying juvenile neuronal ceroid lipofuscinosis. Mol Genet Metab 67:169-75
Das, A M; Jolly, R D; Kohlschutter, A (1999) Anomalies of mitochondrial ATP synthase regulation in four different types of neuronal ceroid lipofuscinosis. Mol Genet Metab 66:349-55
Kay, G W; Hughes, S M; Palmer, D N (1999) In vitro culture of neurons from sheep with Batten disease. Mol Genet Metab 67:83-8
Broom, M F; Zhou, C; Broom, J E et al. (1998) Ovine neuronal ceroid lipofuscinosis: a large animal model syntenic with the human neuronal ceroid lipofuscinosis variant CLN6. J Med Genet 35:717-21
Palmer, D N; Jolly, R D; van Mil, H C et al. (1997) Different patterns of hydrophobic protein storage in different forms of neuronal ceroid lipofuscinosis (NCL, Batten disease). Neuropediatrics 28:45-8
Palmer, D N; Tyynela, J; van Mil, H C et al. (1997) Accumulation of sphingolipid activator proteins (SAPs) A and D in granular osmiophilic deposits in miniature Schnauzer dogs with ceroid-lipofuscinosis. J Inherit Metab Dis 20:74-84
Palmer, D N; Hay, J M (1996) The neuronal ceroid lipofuscinoses (Batten disease): a group of lysosomal proteinoses. Adv Exp Med Biol 389:129-36
Buzy, A; Ryan, E M; Jennings, K R et al. (1996) Use of electrospray ionization mass spectrometry and tandem mass spectrometry to study binding of F0 inhibitors to ceroid lipofuscinosis protein, a model system for subunit c of mitochondrial ATP synthase. Rapid Commun Mass Spectrom 10:790-6
Palmer, D N; Bayliss, S L; Westlake, V J (1995) Batten disease and the ATP synthase subunit c turnover pathway: raising antibodies to subunit c. Am J Med Genet 57:260-5

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