Funding Agency

Agency
National Institute of Health (NIH)
Institute
National Institute of Neurological Disorders and Stroke (NINDS)
Type
Research Project (R01)
Project #
5R01NS032424-03
Application #
2270611
Study Section
Neurological Sciences Subcommittee 1 (NLS)
Project Start
1994-09-30
Project End
1997-08-31
Budget Start
1996-09-01
Budget End
1997-08-31
Support Year
3
Fiscal Year
1996
Total Cost
Indirect Cost

  Institution

Name
University of Helsinki
Department
Type
DUNS #
City
Helsinki
State
Country
Finland
Zip Code
00014

  Publications

Tyynela, J; Sohar, I; Sleat, D E et al. (2001) Congenital ovine neuronal ceroid lipofuscinosis--a cathepsin D deficiency with increased levels of the inactive enzyme. Eur J Paediatr Neurol 5 Suppl A:43-5
Palmer, D N; Tyynela, J; van Mil, H C et al. (1997) Accumulation of sphingolipid activator proteins (SAPs) A and D in granular osmiophilic deposits in miniature Schnauzer dogs with ceroid-lipofuscinosis. J Inherit Metab Dis 20:74-84
Tyynela, J; Suopanki, J; Santavuori, P et al. (1997) Variant late infantile neuronal ceroid-lipofuscinosis: pathology and biochemistry. J Neuropathol Exp Neurol 56:369-75
Tyynela, J; Suopanki, J; Baumann, M et al. (1997) Sphingolipid activator proteins (SAPs) in neuronal ceroid lipofuscinoses (NCL). Neuropediatrics 28:49-52
Tyynela, J; Baumann, M; Henseler, M et al. (1995) Sphingolipid activator proteins (SAPs) are stored together with glycosphingolipids in the infantile neuronal ceroid-lipofuscinosis (INCL). Am J Med Genet 57:294-7
Tyynela, J; Baumann, M; Henseler, M et al. (1995) Sphingolipid activator proteins in the neuronal ceroid-lipofuscinoses: an immunological study. Acta Neuropathol (Berl) 89:391-8
Haltia, M; Tyynela, J; Baumann, M et al. (1995) Immunological studies on sphingolipid activator proteins in the neuronal ceroid-lipofuscinoses. Gerontology 41 Suppl 2:239-48